Distribution of Stiffness Index

Use: To assess the distribution of stiffness

0 - Absent stiffness
1 - Stiffness in face
2 - Stiffness in arms
3 - Stiffness in upper trunk
4 - Stiffness in abdomen
5 - Stiffness in lower trunk
6 - Stiffness in legs
The presence of each item adds one point (maximum score 6)
Intensity of stiffness scale is sometimes used as an ancillary scale to enhance the information.
0 (absent), 1 (mild), 2 (moderate), 3 (severe)
References:
  1. Dalakas MC, Fujii M, Li M, et al. High-dose intravenous immune globulin for stiff-person syndrome. N Engl J Med. 2001;345:1870–1876.
  2. Dalakas MC, Rakocevic, G., Dambrosia J.M., Alexopoulos, H. and McElroy, B. A Double-Blind, Placebo-Controlled Study of Rituximab in Patients with Stiff Person Syndrome. Ann Neurol 2017;82:271-277